Easy, Low Volume, Affordable

A Medical Food for the dietary management of Propionic Acidemia or Vitamin B₁₂ Non-Responsive Methylmalonic Acidemia. Not for the general population of consumers.

A low volume, isoleucine -, methionine-, threonone-, valine free, amino acid based powder for individuals over the age of 1 year with Propionic Acidemia or Vitamin B₁₂ Non-Responsive Methylmalonic Acidemia.

Background

Organic acidemias are inherited metabolic disorders, related to the metabolic pathways of amino acids, carbohydrates, and fatty acids. The most common organic acidemias are propionic acidemia (PPA) and methylmalonic acidemia (MMA). Enzyme defects in degradation of propionyl CoA or methylmalonyl CoA lead to accumulation of these metabolites in the body. The severity of symptoms varies widely, ranging from mild neurological disturbances to metabolic crisis and increased mortality.

comida-OAc datasheet/nutrition information