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A Medical Food for the dietary management of Maple Syrup Urine Disease (MSUD). Not for the general population of consumers.
A low volume, leucine -, isoleucine -, valine free, amino acid based powder for individuals over the age of 1 year with MSUD.
Background
Maple Syrup Urine Disease (MSUD) is an inherited rare disorder in metabolism of the branched chain amino acids Leucine, Isoleucine and Valine, leading to an accumulation of these amino acids and their corresponding oxo acids in all body fluids. If not treated, this condition results in severe irreversible neurological damages and increased mortality.
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Easy, Low Volume, Affordable