Easy, Low Volume, Affordable

A Medical Food for the dietary management of Homocystinuria. Not for the general population of consumers.

A low volume methionine free, concentrated amino acid based powder for individuals over the age of 1 year with vitamin B₆ non-responsive homocystinuria.

Background

Homocystinuria is an inherited rare disorder in metabolism of the amino acid Methionine, caused by a deficiency of the enzyme Cystathione ?-synthetase. If not treated, this will lead to an accumulation of Methionine and Homocysteine in blood and urine, and at the same time to a decrease of Cystine in the body. Without treatment, this condition can result in mental retardation, eye problems and risk of thrombosis.

comida-HCys datasheet/nutrition information