Easy, Low Volume, Affordable

A Medical Food for the dietary management of Glutaric Aciduria Type I. Not for the general population of consumers.

A low volume, lysine free, low in tryptophan amino acid based powder for individuals over the age of 1 year with Glutaric Aciduria Type I.

Background

Glutaric Aciduria Type I is a rare inherited metabolic disorder in protein metabolism, caused by a defect of the enzyme Glutaryl-CoA dehydrogenase, which is responsible for the degradation of the amino acids Lysine, Hydroxylysine and Tryptophan. The consequence is an accumulation of the metabolites Glutaric acid, 3-hydroxyglutaric acid, glutaconic acid and glutaryl¬carnitine in the body, associated with a decrease of carnitine due to increased urinary excretion.

comida-GAc datasheet/nutrition information